临床特点
❖ 儿童多见，本病在成人发病率高于预期，有家族倾 向
❖ 临床表现无特异性，心肌致密化不全患者出现症状 的年龄和临床表现程度个体差异很大，从无症状到 严重心功能不全，或发生猝死
❖ 虽然心肌致密化不全是先天性心肌病，但心脏病症 状的出现常在成年
临床特点
❖ Demographic characteristics of 53 patients Male gender 25 (47.2%)
anterior and anterolateral
segments
超声诊断
超声诊断-三维超声
超声诊断
Two-dimensional apical 4 chamber and parasternal short axis images at the level of the ventricles show dilatation of both ventricles, multiple trabeculae and intertrabecular recesses in inferior, lateral, anterior walls, middle and apical portions of the septum and apex of the left ventricle. A mild pericardial effusion can be observed
❖ Duration 7 ±5 months( range 1–24) ❖ Prevalence in thБайду номын сангаас INCICh 4/10,000/5 years
临床特点
Clinical and electrocardiographic characteristics IN 53 CASES OF NVM ❖ Precordial pain 11 （21%） ❖ Syncope 5 （9.4%） ❖ NYHA Functional class I/II 40 （75%） ❖ NYHA Functional class III/IV 13 （25%） ❖ Familiar occurrence 16 （30.2%） ❖ Cardiac Rhythm
